[Late onset lens particle glaucoma in Marfan syndrome].

نویسندگان

  • E Arranz-Marquez
  • B Fatela-Cantillo
  • M Figueroa
  • M Á Teus
چکیده

CASE REPORT A case is presented of an acute onset lens particle glaucoma originating from a crystalline lens spontaneously dislocated into the vitreous for more than 20 years in a patient diagnosed with Marfan syndrome. DISCUSSION Marfan syndrome is a connective tissue disorder with autosomal dominant inheritance caused by fibrillin gene mutation. Ectopia lentis is the predominant ocular abnormality and a major diagnostic criterion. An association between Marfan syndrome and glaucoma has also been demonstrated. The reported case is unusual in that a complete spontaneous lens dislocation to vitreous was present and progressed to secondary lens particle open angle glaucoma.

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عنوان ژورنال:
  • Archivos de la Sociedad Espanola de Oftalmologia

دوره 90 1  شماره 

صفحات  -

تاریخ انتشار 2015